International Society of Ultrasound in Obstetrics and Gynecology (ISUOG) 122 Freston Road, London W10 6TR, UK Tel: +44 (0) 20 7471 9955 / Fax: +44 (0) 20 7471 9959 Scimitar syndrome (SS) is a rare congenital anomaly characterized by a partial (usually the right lower lobe) or complete unilateral anomalous pulmonary venous drainage in association with ipsilateral lung hypoplasia. The ‘scimitar’ sign is a characteristic chest roentgenographic finding of a crescent-like shadow in the right lower lung field that is produced by the anomalous venous channel. T2/STIR: individual lesions are high signal 1,4. June 2014; Cardiology in the Young 25(03):1-4 ... (Fig. A “sign” is a term for a radiological appearance that suggests the presence of a condition (or disease). } When the lesions are large, they can have a multi-loculated appearance, and can displace the artery to one side - the so-called scimitar sign 4. Abdominal ultrasound, transthoracic echocardiography and computerized tomographic angiography confirmed the presence of Scimitar vein and associated dextro-position of the heart, hypoplastic right lung, hypoplastic right pulmonary artery, secundum atrial septal defect with bidirectional shunt, patent ductus arteriosus, pulmonary hypertension, left superior vena cava, and systemic collateral arteries … Treatment of CAD can be done via surgical resection or percutaneous intervention such as aspiration. Eponym. The lemon sign is seen on axial imaging (usually antenatal ultrasound, although antenatal MRI will also demonstrate this sign) through the head and relates to concavity (not just flattening) of the frontal bones. Scimitar syndrome is a rare association of congenital cardiopulmonary anomalies characterized by an anomalous pulmonary vein (scimitar vein) that drains into the inferior vena cava, a hypogenetic right lung, and dextroposition of the heart. When present, one may rule out a transudative effusion, and should be highly suspicious of a haemothorax as the likely aetiology. Quoad sign 5. Scimitar sign: anomalous pulmonary venous drainage; Seagull sign: respiratory motion artefact; Snoopy sign: congenital absence of the left pericardium; Tadpole appearance: azygous fissure; Tail sign: pulmonary sclerosing pneumocytoma; Takotsubo syndrome; Tracheal and bronchial stenosis: Rat tails and Webs A-line (horizontal artifact) 4. June 2014; Cardiology in the Young 25(03):1-4 Manifestations and clinical course of the syndrome are variable. 5, 19 April 2011 | Congenital Heart Disease, Vol. CAD can rarely recur after treatment. These findings were consistent with the diagnosis of Scimitar syndrome. A similar sonographic appearance is present in haemoperitoneum … ... sign in abdominal tuberculosis, the tadpole sign in breast ultrasound, the ‘elephant on a flagpole sign’ ... † Scimitar sign: anomalous pulmonary venous drainage Alves, P. Veca, G. Borges, C. Monteiro, L. Gra¸ca Ultrasound Unit of the Obstetrics, Gynaecology and P22.08 Reproduction Medicine Department and Unit of Pediatric Meconium peritonitis: prenatal diagnosis and postnatal Surgery, Hospital de Santa Maria, Lisbon, Portugal outcome A 30 year-old secondigravida was referred to our unit at 24 weeks B. Kang of gestation because of an ambiguous genitalia.